The Desmoid Tumor Research Foundation

January 2024

A 10-year-old male with chest wall Desmoid tumor – a rare tumor with unusual presentation

Author Information

Arein A Abufara 1, Qusai A Alsalah 1, Anwar Yousef Jabari 1, Ahmad G Hammouri 2, Mohammad Najajreh 1 3

1Faculty of Medicine, Palestine Polytechnic University, Hebron 9020000, Palestine. 2Radiology Department, Al-Ahli Hospital, Hebron 9020000, Palestine. 3Huda Al Masri Pediatric Cancer Department, Beit Jala Governmental Hospital, Bethlehem 9992100, Palestine.

Publication

J Surg Case Rep

Summary

Desmoid fibromatosis (DF) is a connective tissue tumor that grows aggressively in musculoaponeurotic tissues. It has an annual incidence rate of 2-4/million and is commonly seen in individuals aged 15 to 60 years, with female predominance. While it can occur in any body part, it is commonly found in the extremities, abdominal wall, and abdominal mesentery. But it rarely develops in the chest wall. The cause of the tumor is unknown. However, trauma to the tumor site has been identified in 25% of known cases. The primary treatment is surgical resection. Local recurrence after surgical excision is common. Our study highlights the case of a 12-year-old male patient diagnosed with a desmoid tumor on the chest wall 2 years ago, at the age of 10 years, after mild trauma. The tumor was successfully managed with surgery without radiotherapy treatment and no recurrence was observed in the last 2 years.

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