A rare paediatric mandibular desmoid tumour: emphasis on growth-conscious resection and reconstructive strategy

Summary

Desmoid-type fibromatosis (DTF) of the mandible is a rare, benign histological tumour that behaves aggressively in paediatric patients. We report the case of a 15-year-old boy with a 1-year history of a painless mandibular mass resulting in facial asymmetry. Imaging revealed a large, well-defined lesion of the right mandibular ramus and angle. Incisional biopsy confirmed DTF. Surgical resection was performed via hemimandibulectomy with preservation of the condyle. Immediate reconstruction was achieved using a titanium plate, preserving both facial aesthetics and oral function. Histopathological analysis confirmed complete excision with tumour-free margins. No recurrence was observed at the 12-month follow-up. This case highlights the importance of a growth-sensitive surgical strategy and multidisciplinary collaboration in managing paediatric mandibular DTF.