The Desmoid Tumor Research Foundation

May 2019

Aggressive Fibromatosis in the Mandible of a Child: A Rare Case Report

Author Information

Dinkova AS(1), Atanasov DT(2), Kratunova E(3), Kuzmanov H(1), Kanazirska P(4).

(1)Assist Prof, Dept of Oral Surg, Faculty of Dental Medicine, Medical Univ of Plovdiv, Plovdiv, Bulgaria. (2)Prof and Head, Dept of Oral Surg, Faculty of Dental Medicine, Medical Univ of Plovdiv, Plovdiv, Bulgaria. (3)Clinical AssistProf, Dept of Pediatric Dentistry, College of Dentistry, Univ of Illinois at Chicago, Chicago, IL, USA. (4)Assist Prof, Dept of Imaging Diagnostics, Dental Allergology and Physiotherapy, Medical Univ of Plovdiv, Plovdiv, Bulgaria.

Publication

J Dent Child (Chic)

Summary

Fibromatoses with onset in infancy and childhood are characterized with higher cellularity and more aggressive growth. The mainstream management of aggressive fibromatosis (AF) is surgical removal with microscopically lesion-free margins. In advanced cases, radical surgery can lead to function loss and disfigurement. Hence, early diagnosis and management can avoid complications. Although uncommon (two to four cases per million per year are reported), approximately 25 percent of AF incidents occur in children younger than 15 years of age. Pediatric dentists are likely to be the first practitioners to encounter new cases of AF in younger populations and should have knowledge and understanding of this entity. The purpose of this report is to present a rare case of AF affecting the mandible of a young patient.

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