The Desmoid Tumor Research Foundation

September 2020

A Large Sporadic Intra-abdominal Desmoid-Type Fibromatosis in a Young Male: A Case Report

Author Information

Sioda NA(1), Wakim AA(1), Wong T(2), Patel(3), Coan K(4), Row D(4).

(1)Creighton Univ School of Medicine, Phoenix, AZ. (2)Dept of Surgery, Creighton Univ Arizona Health Education Alliance, Phoenix, AZ. (3)Dept of Radiation Oncology, St. Joseph's Hospital and Medical Center, Phoenix, AZ. (4)Dept of Surgery, St. Joseph's Hospital and Medical Center, Phoenix, AZ.

Publication

Front Surg

Summary

We present a case of a young male with a sporadic 31 ? 25 ? 12 cm desmoid type fibromatosis (DTF) arising from the ileocolic mesentery that was complicated by mass effect on bowel and intra-abdominal organs requiring surgical intervention. The tumor biopsy confirmed the diagnosis of DTF. No evidence of familial adenomatous polyposis or Gardner syndrome was identified. The tumor was surgically excised and intimately associated with the bowel requiring ileocolonic resection with primary anastomosis. At 3-months follow up, surveillance MRI showed no residual or recurrent lesion. A multi-disciplinary approach to this patient's diagnosis and treatment allowed for an accurate diagnosis, efficient treatment, and follow up plan.

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