The Desmoid Tumor Research Foundation

March 2020

Desmoid Type Fibromatosis of the Breast Masquerading as Breast Carcinoma: Value of Dynamic Magnetic Resonance Imaging and its Correlation (ENTIRE ARTICLE)

Author Information

Yong Teoh S(1), Rahmat K(1), Jayalakshmi P(3), Ramli MT(4), Lin Ng W(1), Hoong See M(2), Sze Teh M(2), Vijayananthan A(1).

(1)Dept of Biomedical Imaging, Faculty of Medicine, Univ of Malaya, Kuala Lumpur, Malaysia. (2)Breast Unit Dept of Surgery, Faculty of Medicine, Univ of Malaya, Kuala Lumpur, Malaysia. (3)Dept of Pathology, Faculty of Medicine, Univ of Malaya, Kuala Lumpur, Malaysia. (4)Radiology Dept, Univ Teknologi MARA, Selangor, Malaysia.

Publication

Eur J Breast Health

Summary

Desmoid type fibromatosis of the breasts is a rare stromal tumour of the breast that constitutes less than 0.2% of all breast tumours. Bilateral and multi-centric lesions are extremely rare, with only less than 10 cases reported in literatures. Although benign, it is locally aggressive with recurrence in up to almost one-third of the cases. This case of bilateral multi-centric breast fibromatosis was the first case in our centre. 19-year old woman, with a paternal aunt diagnosed with breast cancer at 30-year-old, presented to our institution with the chief complaint of retracted nipples for 1 year, she denied any history of trauma to her chest. Sonography showed bilateral suspicious hypoechoic masses. MRI was performed for further evaluation due to its extensive involvement of both breasts. The aim of this review is to illustrate the main clinical, radiological and histopathological characteristics of this rare disease to increase awareness of this entity and discuss the role of MRI.

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