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The Desmoid Tumor Research Foundation

May 2023

Primary intra-abdominal desmoid fibromatosis associated with familial adenomatous polyposis: A case report.

Author Information

Zhang, Lei; Zheng, Yaotun; Yu, Xiaoqian; Yu, Kang; Zhu, Shengjie

1Department of Hepatobiliary Surgery, Weihai Central Hospital, Weihai, Shandong 264200, P.R. China. 2Department of Anesthesia, Weihai Central Hospital, Weihai, Shandong 264200, P.R. China. 3Department of Obstetrics, Weihai Central Hospital, Weihai, Shandong 264200, P.R. China. 4Department of Research and Development, Tianjin Lianchuang Technology Development Co., Ltd., Tianjin 300000, P.R. China. 5Department of Oncology, Weihai Central Hospital, Weihai, Shandong 264200, P.R. China.

Publication

Exp Ther Med

Summary

Desmoid fibromatosis (DF) is a clonal proliferative disorder of myofibroblasts, which arises, with a low incidence, in soft tissue, including within the abdomen. The incidence of DF is associated with familial adenomatous polyposis (FAP), and is more common following FAP surgery. It is rare for a patient to make his/her first visit to hospital due to DF symptoms associated with FAP. In the present report, a case of mesenteric DF associated with FAP is described. This case also had incomplete intestinal obstruction due to DF. By summarizing previous studies examining DF and FAP treatment, combined with the disease characteristics of this patient, the clinical treatment strategy for DF associated with FAP was explored.

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