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The Desmoid Tumor Research Foundation

March 2018

A case of retroperitoneal desmoid-type fibromatosis that involved the unilateral ureter after gynaecologic surgery

Author Information

Ono H(1), Hori K(1), Tashima L(1), Tsuruta T(1), Nakatsuka SI(2), Ito K(1).

(1)Department of Obstetrics and Gynecology, Kansai Rosai Hospital, Japan. (2)Department of Pathology, Kansai Rosai Hospital, Japan; Department of Diagnostic Pathology and Cytology, Osaka International Cancer Institute, Japan.

Publication

Int J Surg Case Rep

Summary

We encountered a case of retroperitoneal desmoid-type fibromatosis in a 45-year-old woman who presented with chief complaints of stomach ache and vomiting. She underwent total abdominal hysterectomy and left salpingo-oophorectomy due to uterine myoma and a paroophoritic cyst at 42 years of age. Abdominal computed tomography showed a 5 cm left retroperitoneal tumour and severe hydronephrosis of the left kidney. Therefore, we performed tumour resection, right salpingo-oophorectomy, ureterectomy, and ureterocystostomy. The tumour surrounded the left ureter and adhered to the left internal/external iliac artery, rectum, bladder, and the edge of the vagina. Histopathologic examination yielded a diagnosis of retroperitoneal desmoid-type fibromatosis. One month after the operation, transvaginal sonography showed a 2-cm mass in the pelvis. We suspected tumour recurrence and commenced pharmacotherapy with tranilast (300 mg/day, three times per day). Four months after the operation, the mass disappeared.

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