Aggressive intra abdominal fibromatosis in an adolescent girl – An unusual sequelae to ovarian germ cell tumor

Summary

Background: Abdominal fibromatosis presenting as an abdominal mass is a rare occurrence in a gynecological setting. The diagnosis may not be suspected preoperatively and management may be challenging. Case: An 18-year-old girl with ovarian germ-cell malignancy was managed with staging-laparotomy and chemotherapy. She developed a large abdominal mass ten-months later. An abdominopelvic mass (40 × 20cm) was removed at laparotomy. The histopathological diagnosis was intraabdominal fibromatosis. A rapidly growing abdominal mass recurred postoperatively. After discussion with the tumor-board, chemotherapy with methotrexate and vinblastine was started. The tumor was not responsive and the patient succumbed after the second cycle of chemotherapy. Summary and conclusion: Abdominal fibromatosis should be considered among the differential diagnoses of a rapidly growing abdominal mass after resection of an ovarian germ cell tumor.