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The Desmoid Tumor Research Foundation

February 2016

An atypical presentation of small bowel obstruction and perforation secondary to sporadic synchronous intra-abdominal desmoid tumours.

Author Information

Aleksandras Uzkalnis,Mark Wilsher,Michelle Wilkinson,Sala Abdalla

Department of General Surgery, University Hospital Lewisham, High Street, Lewisham, London, SE13 6LH, UK.,Department of General Surgery, University Hospital Lewisham, High Street, Lewisham, London, SE13 6LH, UK. Electronic address: sala3001@doctors.org.uk.,Department of Histopathology, University Hospital Lewisham, High Street, Lewisham, London, SE13 6LH, UK.

Publication

Summary

The authors report a rare case of small bowel obstruction and perforation secondary to sporadic, synchronous intra-abdominal DTs in a 54-year old man with atypical symptoms and no risk factors or family history. In the non-acute setting patients with sporadic intra-abdominal DTs should be managed in a specialist sarcoma unit by a multidisciplinary team. In the presence of FAP or other polyposis syndromes patients with DTs should be managed at a specialist colorectal unit. Emergent presentations require emergency surgery in suitable candidates.

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