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The Desmoid Tumor Research Foundation

February 2019

Desmoid-type fibromatosis arising in a bifid rib chest wall

Author Information

Mori S(1), Noda Y(1), Kato D(1), Hirooka S(2), Ohtsuka T(1).

(1)Div of Thoracic Surgery, Dept of Surgery, The Jikei Univ School of Medicine, 3-25-8 Nishishinbashi, Minatoku, Tokyo, 105-0003, Japan. (2)Dept of Pathology, The Jikei Univ School of Medicine, 3-25-8 Nishishinbashi, Minatoku, Tokyo, Japan.

Publication

Gen Thorac Cardiovasc Surg

Summary

We report a case of desmoid-type fibromatosis arising in a chest wall's bifid rib. A 42-year-old female complained of right chest pain without remarkable medical, traumatic, or familial history. Chest-computed tomography revealed a chest wall tumor located adjacent to a bifid costal cartilage of third rib. We performed chest wall resection of second and third ribs. Pathologically, the tumor was diagnosed a desmoid-type fibromatosis of the chest wall. We surmise mechanical stimulation due to the bifid rib may be related to the occurrence of the tumor. In case of desmoid-type fibromatosis without somatic gene mutation, traumatic history, wound, implants, or use of female hormonal agents, we should search also local congenital abnormality.

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