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The Desmoid Tumor Research Foundation

July 2021

Desmoid-type fibromatosis: toward a holistic management

Author Information

Penel N (1), Kasper B, van Der Graaf W

(1)Medical Oncology Dept Clinical Research Department, Centre Oscar Lambret Lille Univ Medical School, Lille, France Medical Oncology Dept, Sarcoma Unit, Mannheim Univ Medical Center, Univ of Heidelberg, Mannheim, Germany Dept of Medical Oncology, Netherlands Cancer Institute, Amsterdam Dept of Medical Oncology, Erasmus MC Cancer Institute, Erasmus Univ Medical Center, Rotterdam, The Netherlands.

Publication

Curr Opin Oncol

Summary

This review aimed to explore recent data about the management of desmoid-type fibromatosis. Active surveillance with planned MRI is the first-line management in desmoid-type fibromatosis. A site-specific and stepwise approach should be considered for progressive desmoid-type fibromatosis. Further, a risk-benefit analysis that considers the side effects and long-term sequelae should be conducted before deciding to start any treatment. A less aggressive approach should be considered.

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