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The Desmoid Tumor Research Foundation

February 2014

Extra-abdominal desmoid fibromatosis – A sarcoma unit review of practice, long term recurrence rates and survival.

Author Information

C J Richards,C P Esler,N Eastley,R Aujla,R Silk,R U Ashford,T A McCulloch

Leicester Royal Infirmary, University Hospitals of Leicester NHS Trust, Infirmary Square, Leicester LE1 5WW, United Kingdom. Electronic address:cathy.richards@uhl-tr.nhs.uk.,Leicester Royal Infirmary, University Hospitals of Leicester NHS Trust, Infirmary Square, Leicester LE1 5WW, United Kingdom. Electronic address:neastley@doctors.org.uk.,Leicester Royal Infirmary, University Hospitals of Leicester NHS Trust, Infirmary Square, Leicester LE1 5WW, United Kingdom. Electronic address:randeep.aujla@hotmail.co.uk.,Leicester Royal Infirmary, University Hospitals of Leicester NHS Trust, Infirmary Square, Leicester LE1 5WW, United Kingdom; Nottingham City Hospital, Nottingham University Hospitals NHS Trust, Hucknall Road, Nottingham NG5 1PB, United Kingdom. Electronic address:claire.esler@uhl-tr.nhs.uk.,Leicester Royal Infirmary, University Hospitals of Leicester NHS Trust, Infirmary Square, Leicester LE1 5WW, United Kingdom; Nottingham City Hospital, Nottingham University Hospitals NHS Trust, Hucknall Road, Nottingham NG5 1PB, United Kingdom; Academic Orthopaedics, Trauma & Sports Medicine, University of Nottingham, United Kingdom. Electronic address:robert.ashford@sky.com.,Nottingham City Hospital, Nottingham University Hospitals NHS Trust, Hucknall Road, Nottingham NG5 1PB, United Kingdom. Electronic address:Robert.Silk@nuh.nhs.uk.,Nottingham City Hospital, Nottingham University Hospitals NHS Trust, Hucknall Road, Nottingham NG5 1PB, United Kingdom. Electronic address:Tom.McCulloch@nuh.nhs.uk.

Publication

Summary

Desmoid fibromatosis (DF) carries a significant morbidity and a recognised mortality. Despite this there are currently limited diagnostic or treatment algorithms specific to cases of extra-abdominal DF. Historically surgical excision has formed the cornerstone of treatment. Recently however a paradigm shift has meant many practitioners now adopt a more conservative approach, placing emphasis on active surveillance, function preserving resections, and non-surgical oncologic therapies.

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