The Desmoid Tumor Research Foundation

June 2020

Huge mesenteric fibromatosis presenting with intestinal perforation and acute diffuse peritonitis: a case report (ENTIRE ARTICLE)

Author Information

Xu Y(1), Duan Z(2), Hu W(3), Zhu K(2), You J(4), Abe M(5), Chen P(2), Zhang Q(6), Zong L(2,3,7).

(1)Dept of General Surgery, Yizhen PeopleÂ’s Hospital, Clinical Medical College, Yangzhou University, Yangzhou, China. (2)Dept of Gastrointestinal Surgery, Northern Jiangsu PeopleÂ’s Hospital, Clinical Medical College, Yangzhou University, Yangzhou, China. (3)Dept of General Surgery, Changzhi PeopleÂ’s Hospital, The Affiliated Hospital of Changzhi Medical College, Changzhi, China. (4)Dept of Gastrointestinal Surgery, The First Affiliated Hospital of Xiamen University, Teaching Hospital of Fujian Medical University, Xiamen, China. (5)Div for Health Service Promotion, University of Tokyo Hospital, Tokyo, Japan.(6)Dept of Gastrointestinal Surgery, The First PeopleÂ’s Hospital of Dali City, Dali, China. (7)Dept of Colorectal Surgery, The First Affiliated Hospital of Nanjing Medical University, Nanjing, China.

Publication

Transal Cancer Res

Summary

Here we report a case of huge mesenteric fibromatosis who complained a paroxysmal epigastric pain, and CT scan showed a huge mass, pneumoperitoneum and ascites. An urgent laparotomy showed an intro-abdominal mass and perforation locating at the jejunum. Postoperative histology confirmed it to be mesenteric fibromatosis. With one-year follow-up, the patient had no recurrence. We wish to share our treating experience of this interesting case because it did not belong to a typical type but presenting with acute diffuse peritonitis, and total resection and R0 margin is a key to treat acute case.

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