Idiopathic desmoid-type fibromatosis of the pancreatic head: case report and literature review.

Summary

Desmoid-type fibromatosis (DTF) is an uncommon nonmetastatic fibrous neoplasm. We herein report a case of DTF of unknown cause involving the pancreatic head. Pylorus-preserving pancreaticoduodenectomy was performed due to the patient's debilitating symptoms and suspected malignancy. The pathological examination revealed massive fibroblastic proliferation arising from the musculoaponeurotic tissues, consistent with a diagnosis of DTF. Radical resection is recommended as first-line treatment for pancreatic DTF. Long-term follow-up studies are required to establish the prognosis of pancreatic DTF.