(1)King Fahad Hospital of the Univ, Imam Abdulrahman Bin Faisal Univ College of Medicine, Dept of Surgery,
fibromatoses (Desmoid-type) tumour is rare benign fibrous tumours account approximately for 0.03% of all neoplasms. The Pancreas origin of this tumour is even more rarely reported subset with around 5% only. Establishing the diagnosis is fundamentally based on characteristic pathological and immunohistochemical studies. Surgical resection of the tumour is the mainstay of intervention. We aim to report the success in cure a rare and the largest pancreatic desmoid-type intraabdominal fibromatosis.