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The Desmoid Tumor Research Foundation

March 2018

Orbital Desmoid-Type Fibromatosis: A Case Report and Literature Review

Author Information

Moro A(1), De Angelis P(1), Gasparini G(1), Pelo S(1), Petrone G(2), Lucci Cordisco E(3), Garagiola U(4), D'Amato G(1), Saponaro G(1).

(1)Department of Oral and Maxillofacial Surgery, Catholic University of the Sacred Heart Medical School, Rome, Italy. (2)Department of Histopathology and Cytopathology, Catholic University of the Sacred Heart Medical School, Rome, Italy. (3)Department of Genomic Medicine, Catholic University of the Sacred Heart Medical School, Rome, Italy. (4)Department of Orthodontics, University of Milan, Milan, Italy.

Publication

Case Rep Oncol Med

Summary

In this article, a case of a patient in the pediatric age affected by desmoid fibromatosis localized in the orbit is presented. The management of desmoid fibromatosis is based on the function preservation and the maintenance of a good quality of life, but in case of symptomatic patients or aggressive course of the disease or risk of functional damages, the surgical approach may be considered. Therapeutic alternatives to surgical resection are radiotherapy and systemic therapy.

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