The Desmoid Tumor Research Foundation

November 2017

Sonography used in the infantile desmoid fibromatosis of postcricoid area: A case report

Author Information

Xia C(1), Zhu Q(1), Yue C(2), Hu M(1), Li P(3), Li Z(4)

(1)Department of Diagnostic Ultrasound, Beijing Tongren Hospital, Capital Medical University(2)Department of Pathology, Beijing Tongren Hospital, Capital Medical University(3)Department of Otorhinolaryngology Head and Neck Surgery, Beijing Tongren Hospital, Capital Medical University(4)Department of Diagnostic Ultrasound, Beijing Aerospace General Hospital, Beijing, China

Publication

Medicine (Baltimore)

Summary

Infantile desmoid fibromatosis of the postcricoid area is a rare disease and is characterized by a proliferation of fibrous tissue with non-metastasis, local infiltration, and a high rate of recurrence after surgical resection. Currently, ultrasound is scarcely used in the hypopharynx and larynx area. A 4-year-old boy presented with hoarseness, deep voice and snoring for 2-4 years without any surgical history. On sonography, the lesion was found in the postcricoid area, and the left larynx showed impaired mobility in real time observation. Complete excision with a negative margin in this pivotal anatomic area is impossible, and necessitates a long-time surveillance. Local excision was carried out to relieve the upper airway narrowing. Relieved hoarseness and snoring were reported on the latest follow-up. A residual lesion was seen in the surgical bed and maintained a stable extent on ultrasound and MR imaging after a year. Considering the non-radiation merit and diagnostic ability, ultrasonography is advocated as a valuable supplementary imaging method to CT, MR and laryngoscopy in the juvenile larynx and hypopharynx.

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